Resident University of Colorado Denver, Colorado, United States
Disclosure(s):
Nicole L. Wershoven, MD: No relevant relationships to disclose.
Introduction: Pseudomyogenic hemangioendothelioma is a rare vascular tumor that is a newly recognized entity as of 2003 that is predominantly found in the lower limbs of young males. These tumors are challenging to diagnose given the similarity to other tumors such as epithelioid sarcoma, inconspicuous morphologic characteristics, and lack of immunohistochemical features. The treatment of these tumors is still evolving; however the current mainstay is surgical excision and sometimes either chemo- or radiation therapy. Here we describe the first known case of pseudomyogenic hemangioendothelioma with multiple fascial plane involvement of the head and neck. We recommend to the otolaryngology community that pseudomyogenic hemangioendothelioma be recognized as a possible diagnosis for an indistinct tumor of the head and neck.
Methods: Case report from November 2022. Additionally, there is a review a literature of all Pseudomyogenic hemangioendothelioma of the head and neck.
Results: Ongoing study/analysis; 136 cases identified of pseudomyogenic hemangioendothelioma from 2003 to present with < 10% from the head and neck.
Conclusions: Here we present a case report and review of literature of pseudomyogenic hemangioendothelioma of the head and neck. Although this entity is known for being found on the extremities of primarily young men, cases now demonstrate that it can arise from various locations of the head and neck. We recommend to the otolaryngology community that pseudomyogenic hemangioendothelioma be recognized as a possible diagnosis for an indistinct tumor of the head and neck.
